#1
Which body system is primarily affected by cystic fibrosis?
Respiratory system
ExplanationCystic fibrosis predominantly affects the respiratory system, leading to lung complications.
#2
What is the main cause of cystic fibrosis?
Genetic mutation
ExplanationCystic fibrosis is primarily caused by mutations in the CFTR gene.
#3
What dietary recommendation is essential for individuals with cystic fibrosis due to pancreatic insufficiency?
High-calorie diet
ExplanationA high-calorie diet is crucial for individuals with cystic fibrosis to compensate for malabsorption caused by pancreatic insufficiency.
#4
Which of the following is a common symptom of cystic fibrosis in infants?
Salty-tasting skin
ExplanationSalty-tasting skin is a characteristic symptom due to excessive salt in sweat, a hallmark of cystic fibrosis.
#5
What is the gold standard diagnostic test for cystic fibrosis?
Sweat chloride test
ExplanationThe sweat chloride test is considered the gold standard for diagnosing cystic fibrosis, measuring chloride levels in sweat.
#6
What is the typical life expectancy of individuals with cystic fibrosis?
40-50 years
ExplanationThe average life expectancy for cystic fibrosis patients is around 40 to 50 years due to advances in treatment.
#7
Which respiratory complication is commonly associated with cystic fibrosis?
Pneumothorax
ExplanationPneumothorax, or collapsed lung, is a common respiratory complication in cystic fibrosis patients.
#8
Which of the following organs is primarily affected by cystic fibrosis-related diabetes (CFRD)?
Pancreas
ExplanationCystic fibrosis-related diabetes primarily affects the pancreas due to insulin insufficiency or resistance.
#9
What is the recommended frequency of chest physiotherapy for cystic fibrosis patients?
Three times weekly
ExplanationCystic fibrosis patients typically undergo chest physiotherapy three times weekly to help clear mucus from the airways.
#10
Which of the following is NOT a component of cystic fibrosis management?
Beta-blockers
ExplanationBeta-blockers are not typically part of cystic fibrosis management; treatment focuses on respiratory and digestive complications.
#11
What is the role of genetic counseling in cystic fibrosis management?
Assessing the risk of cystic fibrosis in offspring
ExplanationGenetic counseling helps evaluate the risk of cystic fibrosis in future generations and provides information for family planning.
#12
Which of the following medications is commonly used for the treatment of cystic fibrosis-related lung infections?
Antibiotics
ExplanationAntibiotics are frequently prescribed to manage lung infections, a common complication in cystic fibrosis.
#13
Which of the following is a potential complication of cystic fibrosis in the reproductive system?
Infertility
ExplanationInfertility can arise due to obstructed vas deferens or other reproductive complications associated with cystic fibrosis.
#14
What is the primary goal of genetic counseling for cystic fibrosis?
To inform individuals about carrier status and risks
ExplanationGenetic counseling aims to educate individuals about their carrier status and the risks associated with cystic fibrosis.
#15
Which of the following conditions is NOT typically associated with cystic fibrosis?
Chronic obstructive pulmonary disease (COPD)
ExplanationCystic fibrosis is not typically associated with COPD, which is more common in smokers and related to other factors.