#1
Which organ is primarily affected by cystic fibrosis?
Lungs
ExplanationCystic fibrosis primarily affects the respiratory system, leading to lung complications.
#2
What is the underlying cause of cystic fibrosis?
Genetic mutation
ExplanationCystic fibrosis is caused by mutations in the CFTR gene, leading to dysfunctional chloride ion transport.
#3
What percentage of cystic fibrosis cases are diagnosed by age 2 in the United States?
90%
ExplanationApproximately 90% of cystic fibrosis cases are diagnosed by age 2 in the United States, enabling early intervention.
#4
Which of the following is a potential complication of cystic fibrosis-related diabetes?
Hyperglycemia
ExplanationHyperglycemia is a potential complication of cystic fibrosis-related diabetes, affecting blood sugar levels.
#5
Which vitamin absorption is commonly impaired in individuals with cystic fibrosis?
Vitamin D
ExplanationVitamin D absorption is commonly impaired in individuals with cystic fibrosis, leading to potential deficiencies.
#6
Which of the following is NOT a symptom of cystic fibrosis?
Frequent nosebleeds
ExplanationFrequent nosebleeds are not a typical symptom of cystic fibrosis; common symptoms include respiratory and digestive issues.
#7
What is the most common test used to diagnose cystic fibrosis?
Sweat test
ExplanationThe sweat test is the primary diagnostic tool for cystic fibrosis, measuring elevated chloride levels in sweat.
#8
What is the average life expectancy for individuals with cystic fibrosis?
40-50 years
ExplanationThe average life expectancy for individuals with cystic fibrosis is around 40-50 years, though this can vary.
#9
Which of the following is a common complication of cystic fibrosis?
Gastrointestinal obstruction
ExplanationGastrointestinal obstruction is a common complication of cystic fibrosis, affecting the digestive system.
#10
Which of the following is a genetic mutation associated with cystic fibrosis?
CFTR
ExplanationThe CFTR gene mutation is associated with cystic fibrosis, impacting chloride ion transport.
#11
Which of the following treatments is NOT commonly used in cystic fibrosis care?
Insulin therapy
ExplanationInsulin therapy is not a common treatment for cystic fibrosis; treatments focus on respiratory and digestive support.
#12
What is the recommended frequency for pulmonary function tests in cystic fibrosis patients?
Every 3 months
ExplanationPulmonary function tests are recommended every 3 months to monitor respiratory health in cystic fibrosis patients.
#13
Which of the following is a potential complication of long-term antibiotic therapy in cystic fibrosis?
Ototoxicity
ExplanationOtotoxicity, or hearing loss, is a potential complication of long-term antibiotic therapy in cystic fibrosis.
#14
Which of the following respiratory therapies is specifically aimed at loosening mucus in cystic fibrosis patients?
Percussion and postural drainage
ExplanationPercussion and postural drainage are respiratory therapies aimed at loosening mucus in the airways of cystic fibrosis patients.
#15
What is the gold standard treatment for pancreatic insufficiency in cystic fibrosis?
Pancreatic enzyme replacement therapy
ExplanationPancreatic enzyme replacement therapy is the gold standard for treating pancreatic insufficiency in cystic fibrosis.